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Clinics and Practice
Volume 8
Issue 1
10.4081/cp.2018.1004
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Clinics and Practice is published by MDPI from Volume 11 Issue 1 (2021). Previous articles were published by another publisher in Open Access under a CC-BY (or CC-BY-NC-ND) licence, and they are hosted by MDPI on mdpi.com as a courtesy and upon agreement with PAGEPress.
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Case Report

Heterotaxy Syndrome with Intestinal Malrotation, Polysplenia and Azygos Continuity

by
Stéphanie Cupers
1,
Christine Van Linthout
2,
Brigitte Desprechins
3,
Léon Rausin
4,
Martine Demarche
5 and
Marie-Christine Seghaye
1,*
1
Department of Pediatrics, University Hospital Liège, Liège, Belgium
2
Department of Gynecology and Obstetrics, University Hospital Liège, Liège, Belgium
3
Medical Imaging, University Hospital Liège, Liège, Belgium
4
Department of Medical Imaging, Regional Hospital Center La Citadelle, Liège, Belgium
5
Department of Surgery, Regional Hospital Center La Citadelle, Liège, Belgium
*
Author to whom correspondence should be addressed.
Clin. Pract. 2018, 8(1), 1004; https://doi.org/10.4081/cp.2018.1004
Submission received: 11 July 2017 / Revised: 11 July 2017 / Accepted: 1 December 2017 / Published: 8 January 2018

Abstract

Heterotaxy syndrome is a situs anomaly that comprises a large spectrum of cardiac and extracardiac malformations. Its association with intestinal malrotation is frequent. This later might be asymptomatic or manifest by signs of abdominal discomfort or of intestinal obstruction. We report on the case of a full term, small for gestational age neonate in whom heterotaxy syndrome with partial situs inversus abdominalis, intestinal malrotation, polysplenia and vena azygos continuity was diagnosed at prenatal echography. Due to the high risk of volvulus carried by the malrotation, Ladd’s procedure was performed at the age of two months. Follow-up examination at the age of four years shows excellent post-operative result and normal development of the child.
Keywords: heterotaxy; intestinal malrotation; azygos continuity heterotaxy; intestinal malrotation; azygos continuity

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MDPI and ACS Style

Cupers, S.; Van Linthout, C.; Desprechins, B.; Rausin, L.; Demarche, M.; Seghaye, M.-C. Heterotaxy Syndrome with Intestinal Malrotation, Polysplenia and Azygos Continuity. Clin. Pract. 2018, 8, 1004. https://doi.org/10.4081/cp.2018.1004

AMA Style

Cupers S, Van Linthout C, Desprechins B, Rausin L, Demarche M, Seghaye M-C. Heterotaxy Syndrome with Intestinal Malrotation, Polysplenia and Azygos Continuity. Clinics and Practice. 2018; 8(1):1004. https://doi.org/10.4081/cp.2018.1004

Chicago/Turabian Style

Cupers, Stéphanie, Christine Van Linthout, Brigitte Desprechins, Léon Rausin, Martine Demarche, and Marie-Christine Seghaye. 2018. "Heterotaxy Syndrome with Intestinal Malrotation, Polysplenia and Azygos Continuity" Clinics and Practice 8, no. 1: 1004. https://doi.org/10.4081/cp.2018.1004

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